Lymphoedema

Classification

  1. Primary (Milroy's disease)
    • Congenital disease / primary lymphatic failure
    • 3 times more common in women
    • Pathology originates within lymphatics
  2. Secondary
    • Malignant infiltration of nodes
    • Infections - filiaris (Wuchereria Bancrofti worm), TB
    • Post radiotherapy / post surgery - axillary dissection in breast

 

Approach

  • Expose legs
  • Preserve dignity
  1. Inspect

    • Grossly swollen, no particular distribution
    • Tends to be bilateral
    • Note loss of contour of ankle
    • May be lichenified fronds on the toes and skin looks thick and indurated
    • Yellow discolouration of nails
  2. Palpate
    • Determine pitting or non-pitting?
    • Initially oedema characteristically pitting but later stops pitting as tissue resistance increases
    • Palpate groin for inguinal lymphadenopathy
  3. Percuss
  4. Auscultate

Completion

  1. Examine JVP, heart, lungs to exclude Right heart failure
  2. Palpate liver for hepatomegaly
  3. Ask patient to determine any hereditary conditions that predispose to lymphoedema

Differential diagnosis of swollen legs

  1. Central
    • Right heart failure, hypoalbuminaemia, nephrotic syndrome, hypothyroidism
  2. Peripheral
    • Klippel-Trenaunay syndrome, chronic venous insufficiency, post phlebitic limb
  3. Rare
    • AV malformations (Parkes-Weber)

Treatment options for lymphoedema

  1. Non-surgical
    • Grade III compression stockns
    • Intermittend pneumatic compression device
    • Leg elevation (reduces intravascular hydrostatic pressure and stockings increase extracellular hydrostatic pressure)
  2. Surgical
    • Rarely used - results tend to be poor
    • Likely to be successful where there is discreet occlusion of lymphatics
    • Options: lymphovenous anastamosis, debulking of leg