Immunodeficiency

Body's defences

  1. Innate
    • Skin
    • Complement
  2. Interactive
    • Cellular
    • Antibody 

Immunisation

  1. Active or Passive
    • Active: pre-formed antibodies (HBsAG, immunocompromised patients with shingles, botulism, rabies)
    • Passive: transplacental transfer of IgG protects for first 6 months of life
  2. Natural or artificial 
    • Natural: following infection
    • Following vaccination

Different types of vaccinations

  1. Live attenuated: - BCG, sabine for polio, MMR
    • Long lasting immunity
    • Potentially dangerous in immunocompromised patients
  2. Killed organisms: typhoid, cholera, pertussis
    • Smaller immune response: usually boosters are required
  3. Toxoid
    • Not the infection but the effects of toxin that result from infection (eg. Tetanus toxoid)
  4. Other bacterial constiuents 
    • Surface polysaccharides and proteins

Immunoglobulin

  1. Antigen binding sites (light and heavy chain regions)
  2. Complement activation parts
  3. Immune adherence
  4. Heavy chains determine the class of immunoglobulin - GAMDE
  5. Light chains are kappa- or lambda- irrespective of the immunoglobulin class
  • IgG: most important Monomeric: activates complement, binds to killer t-cells
  • IgA: present in secretions of BIT, respiratory tract; Dimer with J-chain
  • IgM: Largest - Pentamer
  • IgE: Monomer bound to mast cells

Immunodeficiency

  1. Acquired
    • Drugs
    • Infections
  2. Congenital
    1. Bruton's X-linked gammopathy
    2. T-cells: Thymic atrophy in Di-George anomaly
    3. SCID
    4. Lymphoma

 

 

Infections in Compromised patients

  1. Congenital
    • Bruton type hypogammaglobulinaemia
    • Di George type
    • Combined
    • Deficiency of neutrophil function in chronic granulomatous disease 
  2. Acquired
    • Infections: AIDS
    • Drugs: steroids, cytotoxics
    • Diabetes (also because glucose as a culture medium in urine and on skin)
    • Instrumentation - lines, catheters, ventilation
    • Prosthesis: hips, knees, heart valves

 

Sources of infection

  1. Endogenous
    • Colonic bacteria
    • GIT
    • Skin
  2. Exogenous
    • Foamites
    • Other people
    • Transplanted tissues
    • "Opportunist"